Surgical treatment of penoscrotal lymphedema in a patient with Milroy’s disease: case report

Introduction: Milroy disease manifests itself as lymphedema of the lower limbs and genital region, which causes physical and social damage. Case Report: A case of severe-scrotal lymphedema in a patient with Milroy disease. Surgical resection of the affected tissue and reco...

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Main Authors: João Roberto Farias de Souza, Maria Luiza Marialva Rodrigues, Sérgio Antônio Saldanha Rodrigues Tamborini, Lívia Dornelas Côrrea, Clarissa Leite Turrer, Armando Chiari
Format: Article
Language:English
Published: Thieme Revinter Publicações Ltda. 2022-06-01
Series:Revista Brasileira de Cirurgia Plástica
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Online Access:http://www.rbcp.org.br/export-pdf/3136/en_v37n2a18.pdf
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Summary:Introduction: Milroy disease manifests itself as lymphedema of the lower limbs and genital region, which causes physical and social damage. Case Report: A case of severe-scrotal lymphedema in a patient with Milroy disease. Surgical resection of the affected tissue and reconstruction with local flaps and skin graft were performed. Discussion: Milroy disease is a rare autosomal dominant disease. The clinical presentation is progressive and results from hypoplasia of the lymphatic vessels of the lower limbs. Treatment in advanced cases is mainly surgical. Conclusion: In the case of a patient with Milroy disease and severe penoscrotal lymphedema, surgical treatment is a good option. The use of parascrotal flaps for scrotoplasty associated with a graft to recover the penis provides a good functional result.
ISSN:1983-5175
2177-1235