Surgical treatment of penoscrotal lymphedema in a patient with Milroy’s disease: case report
Introduction: Milroy disease manifests itself as lymphedema of the lower limbs and genital region, which causes physical and social damage. Case Report: A case of severe-scrotal lymphedema in a patient with Milroy disease. Surgical resection of the affected tissue and reco...
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Main Authors: | , , , , , |
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Format: | Article |
Language: | English |
Published: |
Thieme Revinter Publicações Ltda.
2022-06-01
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Series: | Revista Brasileira de Cirurgia Plástica |
Subjects: | |
Online Access: | http://www.rbcp.org.br/export-pdf/3136/en_v37n2a18.pdf |
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Summary: | Introduction:
Milroy disease manifests itself as lymphedema of the lower limbs and genital region, which causes physical and social damage.
Case Report:
A case of severe-scrotal lymphedema in a patient with Milroy disease. Surgical resection of the affected tissue and reconstruction with local flaps and skin graft were performed.
Discussion:
Milroy disease is a rare autosomal dominant disease. The clinical presentation is progressive and results from hypoplasia of the lymphatic vessels of the lower limbs. Treatment in advanced cases is mainly surgical.
Conclusion:
In the case of a patient with Milroy disease and severe penoscrotal lymphedema, surgical treatment is a good option. The use of parascrotal flaps for scrotoplasty associated with a graft to recover the penis provides a good functional result. |
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ISSN: | 1983-5175 2177-1235 |