Juvenile Systemic Sclerosis Presenting With Severe Pulmonary Vascular Disease: ECMO Stabilization During Aggressive Therapy Resulting in a Favorable Outcome

Juvenile Systemic Sclerosis Presenting With Severe Pulmonary Vascular Disease: ECMO Stabilization During Aggressive Therapy Resulting in a Favorable Outcome

ABSTRACT Juvenile systemic sclerosis (jSSc) associated pulmonary hypertension (PH) is rare, but, the leading cause of morbidity and mortality in jSSc. This is a case of a 10‐year‐old girl whose initial presentation of positive U3‐RNP antibody jSSc included diffuse skin findings, severe pulmonary art...

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Bibliographic Details
Main Authors: Stephanie M. Tsoi, Shannon Cheung, Roberto Alejandro Valdovinos, Elena Amin, Hythem Nawaytou, Elizabeth Colglazier, Claire Parker, April Edwell, Susan Kim, Jeffrey R. Fineman
Format: Article
Language:English
Published: Wiley 2025-04-01
Series:Pulmonary Circulation
Subjects:
extracorporeal membranous oxygenation
juvenile systemic sclerosis
pediatric critical care
pulmonary hypertension
right ventricular failure
Online Access:https://doi.org/10.1002/pul2.70106
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https://doi.org/10.1002/pul2.70106

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