Unraveling the complexity of IgG4-related aortitis and periarteritis: from pathogenesis to clinical practice

IgG4-related disease (IgG4-RD) is a chronic fibrotic inflammatory condition characterized by elevated serum IgG4 levels and the infiltration of IgG4-bearing plasma cells in affected organs. It can involve various organs, particularly large vessels. IgG4-related aortitis/periaortitis and periarteriti...

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Bibliographic Details
Main Authors: Yan Wang, Feng Tian, Hui Li
Format: Article
Language:English
Published: Frontiers Media S.A. 2025-07-01
Series:Frontiers in Immunology
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Online Access:https://www.frontiersin.org/articles/10.3389/fimmu.2025.1625456/full
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