Pemphigus Herpetiformis in Childhood: Clinical Case
Background. Pemphigus herpetiformis is a rare atypical bullous dermatosis of autoimmune nature. It is characterized by rashes in the form of plaques with papules and vesicles at peripheral areas, or in the form of grouped papules, vesicles or tense bubbles with clinical similarity to During's h...
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| Format: | Article |
| Language: | English |
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"Paediatrician" Publishers LLC
2023-11-01
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| Series: | Вопросы современной педиатрии |
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| Online Access: | https://vsp.spr-journal.ru/jour/article/view/3308 |
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| author | Nikolay N. Murashkin Alexander I. Materikin Roman V. Epishev Maria A. Leonova Leonid A. Opryatin Dmitri V. Fedorov Roman A. Ivanov Alena A. Savelova Oksana R. Katunina Kirill A. Kulikov Ilgiz I. Yarullin |
| author_facet | Nikolay N. Murashkin Alexander I. Materikin Roman V. Epishev Maria A. Leonova Leonid A. Opryatin Dmitri V. Fedorov Roman A. Ivanov Alena A. Savelova Oksana R. Katunina Kirill A. Kulikov Ilgiz I. Yarullin |
| author_sort | Nikolay N. Murashkin |
| collection | DOAJ |
| description | Background. Pemphigus herpetiformis is a rare atypical bullous dermatosis of autoimmune nature. It is characterized by rashes in the form of plaques with papules and vesicles at peripheral areas, or in the form of grouped papules, vesicles or tense bubbles with clinical similarity to During's herpetiformis dermatitis. Pemphigus herpetiformis diagnosis in pediatric practice is difficult due to the similarity of clinical manifestations to bullous dermatoses of other etiology, the rarity of the disease in children, and small number of scientific publications.Clinical case description. Clinical case of pemphigus herpetiformis in a child is described. All necessary diagnostic algorithms for diagnosis and therapeutic tactics for patient management are presented. Dapsone and prednisolone were used as first-line drugs during the patient's treatment. They have shown its efficacy in management of such patients.Conclusion. Differential diagnosis of pemphigus herpetiformis and other bullous dermatoses in children is presented. The results of successful drug treatment are shown. |
| format | Article |
| id | doaj-art-b31d8a28eaa44b8eaada84cb381ddcbc |
| institution | Matheson Library |
| issn | 1682-5527 1682-5535 |
| language | English |
| publishDate | 2023-11-01 |
| publisher | "Paediatrician" Publishers LLC |
| record_format | Article |
| series | Вопросы современной педиатрии |
| spelling | doaj-art-b31d8a28eaa44b8eaada84cb381ddcbc2025-08-04T13:09:42Zeng"Paediatrician" Publishers LLCВопросы современной педиатрии1682-55271682-55352023-11-0122545846310.15690/vsp.v22i5.26362131Pemphigus Herpetiformis in Childhood: Clinical CaseNikolay N. Murashkin0Alexander I. Materikin1Roman V. Epishev2Maria A. Leonova3Leonid A. Opryatin4Dmitri V. Fedorov5Roman A. Ivanov6Alena A. Savelova7Oksana R. Katunina8Kirill A. Kulikov9Ilgiz I. Yarullin10National Medical Research Center of Children’s Health; Sechenov First Moscow State Medical University; Central State Medical Academy of Department of Presidential AffairsNational Medical Research Center of Children’s HealthNational Medical Research Center of Children’s HealthNational Medical Research Center of Children’s HealthNational Medical Research Center of Children’s HealthNational Medical Research Center of Children’s HealthNational Medical Research Center of Children’s HealthNational Medical Research Center of Children’s HealthNational Medical Research Center of Children’s HealthNational Medical Research Center of Children’s HealthCentral State Medical Academy of Department of Presidential AffairsBackground. Pemphigus herpetiformis is a rare atypical bullous dermatosis of autoimmune nature. It is characterized by rashes in the form of plaques with papules and vesicles at peripheral areas, or in the form of grouped papules, vesicles or tense bubbles with clinical similarity to During's herpetiformis dermatitis. Pemphigus herpetiformis diagnosis in pediatric practice is difficult due to the similarity of clinical manifestations to bullous dermatoses of other etiology, the rarity of the disease in children, and small number of scientific publications.Clinical case description. Clinical case of pemphigus herpetiformis in a child is described. All necessary diagnostic algorithms for diagnosis and therapeutic tactics for patient management are presented. Dapsone and prednisolone were used as first-line drugs during the patient's treatment. They have shown its efficacy in management of such patients.Conclusion. Differential diagnosis of pemphigus herpetiformis and other bullous dermatoses in children is presented. The results of successful drug treatment are shown.https://vsp.spr-journal.ru/jour/article/view/3308pemphigus herpetiformisdiagnosisindirect immunofluorescence testtreatmentdapsoneprednisolonechildrenbullous dermatosis |
| spellingShingle | Nikolay N. Murashkin Alexander I. Materikin Roman V. Epishev Maria A. Leonova Leonid A. Opryatin Dmitri V. Fedorov Roman A. Ivanov Alena A. Savelova Oksana R. Katunina Kirill A. Kulikov Ilgiz I. Yarullin Pemphigus Herpetiformis in Childhood: Clinical Case Вопросы современной педиатрии pemphigus herpetiformis diagnosis indirect immunofluorescence test treatment dapsone prednisolone children bullous dermatosis |
| title | Pemphigus Herpetiformis in Childhood: Clinical Case |
| title_full | Pemphigus Herpetiformis in Childhood: Clinical Case |
| title_fullStr | Pemphigus Herpetiformis in Childhood: Clinical Case |
| title_full_unstemmed | Pemphigus Herpetiformis in Childhood: Clinical Case |
| title_short | Pemphigus Herpetiformis in Childhood: Clinical Case |
| title_sort | pemphigus herpetiformis in childhood clinical case |
| topic | pemphigus herpetiformis diagnosis indirect immunofluorescence test treatment dapsone prednisolone children bullous dermatosis |
| url | https://vsp.spr-journal.ru/jour/article/view/3308 |
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