Angiomatoid fibrous histiocytoma â an adolescent with an unusual presentation and course
Introduction: Angiomatoid fibrous histiocytoma is a rare soft tissue neoplasm, which usually presents as an indolent mass in children and young adults and is often mistaken for a hematoma or hemangioma. Suspecting this diagnosis from imaging findings may be challenging, leading to diagnostic delays....
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| Main Authors: | , , , , |
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| Format: | Article |
| Language: | English |
| Published: |
Publicaciones Permanyer
2025-07-01
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| Series: | Portuguese Journal of Pediatrics |
| Subjects: | |
| Online Access: | https://pjp.spp.pt/frame_eng.php?id=114 |
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| Summary: | Introduction: Angiomatoid fibrous histiocytoma is a rare soft tissue neoplasm, which usually presents as an indolent mass in children and young adults and is often mistaken for a hematoma or hemangioma. Suspecting this diagnosis from imaging findings may be challenging, leading to diagnostic delays. Prognosis is generally favorable and metastases are infrequent at presentation. Case report: We describe the case of an adolescent who presented with a two-month history of a growing mass in the left scapular region, where diagnosis was made possible through surgical biopsy. Discussion: There were loco-regional lymphatic invasions and lung metastases at admission, and despite surgery and chemotherapy the disease rapidly progressed to death.
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| ISSN: | 2184-4453 |