Generation and characterisation of four human NAD(P)HX epimerase (NAXE) knockout iPSC lines

Pathogenic variants in NAD(P)HX epimerase (NAXE) cause early-onset progressive encephalopathy with brain edema and/or leukoencephalopathy-1 (PEBEL1), an ultra-rare severe neurometabolic disorder resulting in death in infancy. The absence of functional NAD(P)HX epimerase leads to accumulation of S- a...

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Bibliographic Details
Main Authors: Tim Sikora, Myrto Patraskaki, Sara Howden, Alison Graham, John Christodoulou, Carole L. Linster, Nicole J. Van Bergen
Format: Article
Language:English
Published: Elsevier 2025-09-01
Series:Stem Cell Research
Online Access:http://www.sciencedirect.com/science/article/pii/S1873506125001321
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